Vasculitis represents a clinically heterogenous group of diseases of multifactorial etiology characterized by inflammation of either large-sized vessels (large-vessel vasculitis, e.g. Giant-cell arteritis and Takayasu arteritis), medium-sized vessels (medium-vessel vasculitis e.g. polyarteritis nodosa and Kawasaki disease), or small-sized vessels (small-vessel vasculitis, e.g. granulomatosis with polyangiitis, microscopic polyangiitis, immunoglobulin A vasculitis, and cutaneous leukocytoclastic angiitis). Vasculitis occurs at any age, may be acute or chronic, and manifests with general symptoms such as fever, weight loss and fatigue, as well as more specific clinical signs depending on the type of vessels and organs affected. The degree of severity is variable, ranging from life or sight threatening disease (e.g. Behcet disease) to relatively minor skin disease. [ Orphanet:52759 ]
Term information
- SCTID:31996006 (MONDO:equivalentTo)
- NCIT:C26912 (MONDO:exact-label-match)
- Orphanet:52759 (MONDO:equivalentTo)
- MedDRA:10036023 (Orphanet:52759/e)
- EFO:0006803 (MONDO:equivalentTo)
- icd11.foundation:572581721 (Orphanet:52759)
- Wikipedia:Vasculitis (EFO:0006803)
- UMLS:C0042384 (Orphanet:52759/e)
- MESH:D014657 (Orphanet:52759/e)
- GARD:18844 (Orphanet:52759)
- MedDRA:10047115 (Orphanet:52759/e)
- DOID:865 (MONDO:equivalentTo)
gard_rare, otar, disease_grouping, rare, ordo_group_of_disorders
http://linkedlifedata.com/resource/umls/id/C0042384
http://identifiers.org/snomedct/31996006
http://purl.obolibrary.org/obo/NCIT_C26912
http://purl.obolibrary.org/obo/DOID_865
http://identifiers.org/mesh/D014657
http://www.orpha.net/ORDO/Orphanet_52759