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diffuse cutaneous mastocytosis

Go to external page http://purl.obolibrary.org/obo/MONDO_0019315

Diffuse cutaneous mastocytosis (DCM) is a rare form of cutaneous mastocytosis (CM) characterized by generalized erythroderma, various degrees of blistering, skin with a ''peau d'orange'' appearance and the accumulation of mast cells in the skin. At least two DCM variants are recognized, one with extreme blistering (Bullous DCM) and one with infiltrations (Pseudoxanthomatous DCM). [ Orphanet:79456 ]

Synonyms: diffuse cutaneous mastocytosis diffuse cutaneous maculopapulous mastocytosis

This is just here as a test because I lose it

Term information

database cross reference
  • ICDO:9740/1 (NCIT:C3218)
  • NCIT:C3218 (MONDO:equivalentTo)
  • Orphanet:79456 (MONDO:equivalentTo)
  • GARD:12686 (MONDO:GARD)
  • MEDGEN:44303 (MONDO:equivalentTo)
  • UMLS:C0024901 (MONDO:equivalentTo)
  • DOID:3665 (MONDO:equivalentTo)
  • MedDRA:10012812 (Orphanet:79456/e)
Subsets

ordo_disorder, gard_rare, rare, nord_rare, orphanet_rare

closeMatch

http://identifiers.org/meddra/10012812

exactMatch

http://www.orpha.net/ORDO/Orphanet_79456

http://identifiers.org/medgen/44303

http://purl.obolibrary.org/obo/DOID_3665

http://linkedlifedata.com/resource/umls/id/C0024901

http://purl.obolibrary.org/obo/NCIT_C3218

id

MONDO:0019315

Term relations

Subclass of: