Type 1 autoimmune pancreatitis is a form of autoimmune pancreatitis seen in elderly males (>60 years) and presenting with abdominal pain, steatorrhea, obstructive jaundice and other organ (bile duct, kidneys and retroperitoneum) involvement. It is thought to be due to an immunoglobulin G4 (IgG4)-associated systemic disease. [ Orphanet:280302 ]
Synonyms: IgG4-related pancreatitis lymphoplasmacytic sclerosing pancreatitis autoimmune pancreatitis type 1 AIP type 1
Term information
- GARD:21076 (MONDO:GARD)
- UMLS:C4302243 (MONDO:equivalentTo)
- SCTID:722872000 (MONDO:equivalentTo)
- Orphanet:280302 (MONDO:equivalentTo)
- MEDGEN:927912 (MONDO:equivalentTo)
- PMID:25985088 (EFO:1000780)
- EFO:1000780 (MONDO:equivalentTo)
gard_rare, otar, ordo_subtype_of_a_disorder, rare, nord_rare
http://identifiers.org/medgen/927912
http://identifiers.org/snomedct/722872000
http://linkedlifedata.com/resource/umls/id/C4302243
http://www.orpha.net/ORDO/Orphanet_280302