congenital pulmonary airway malformation

Go to external page http://purl.obolibrary.org/obo/MONDO_0016580


An abnormality in lung development that is characterized by a multicystic mass resulting from an adenomatous overgrowth of the terminal bronchioles with a consequent reduction of pulmonary alveoli. This anomaly is classified into three types by the cyst size. [ MESH:D015615 ]

Synonyms: CCAM CPAM congenital cystic adenomatoid malformation of lung congenital cystic adenomatoid malformation of the lung congenital cystic adenomatous malformation of the lung congenital cystic disease of the lung

This is just here as a test because I lose it

Term information

database cross reference
  • SCTID:111318005 (MONDO:equivalentTo)
  • UMLS:C0010668 (MONDO:equivalentTo)
  • Orphanet:2444 (MONDO:equivalentTo)
  • GARD:18772 (MONDO:GARD)
  • MESH:D015615 (MONDO:equivalentTo)
  • icd11.foundation:2091138945 (https://orcid.org/0000-0002-4142-7153)
  • NCIT:C98892 (MONDO:equivalentTo)
  • MEDGEN:8225 (MONDO:equivalentTo)
Subsets

gard_rare, ordo_disorder, rare, ordo_malformation_syndrome, nord_rare, orphanet_rare

IAO 0000233

https://github.com/monarch-initiative/mondo/issues/6876

https://github.com/monarch-initiative/mondo/issues/4069

https://github.com/monarch-initiative/mondo/issues/6754

exactMatch

http://purl.obolibrary.org/obo/NCIT_C98892

http://identifiers.org/medgen/8225

http://linkedlifedata.com/resource/umls/id/C0010668

http://www.orpha.net/ORDO/Orphanet_2444

http://identifiers.org/snomedct/111318005

http://identifiers.org/mesh/D015615

has related synonym

cystic adenomatoid malformation of lung

congenital cystic adenomatoid malformation

id

MONDO:0016580