Dermatitis herpetiformis (DH) is a chronic autoimmune subepidermal bullous disease characterized by grouped pruritic lesions such as papules, urticarial plaques, erythema, and herpetiform vesiculae, with a predominantly symmetrical distribution on extensor surfaces of the elbows (90%), knees (30%), shoulders, buttocks, sacral region, and face of children and adults. Erosions, excoriations and hyperpigmentation usually follow. DH may also appear as a consequence of gluten intolerance. [ Orphanet:1656 ]
Synonyms: Durhing-Brocq disease Duhring's disease dermatosis herpetiformis dermatitis herpetiformis
Term information
- ICD10CM:L13.0 (Orphanet:1656/e)
- MESH:D003874 (Orphanet:1656/e)
- MedDRA:10012468 (Orphanet:1656/e)
- UMLS:C0011608 (MONDO:equivalentTo)
- icd11.foundation:286313127 (Orphanet:1656)
- Wikipedia:Dermatitis_herpetiformis (EFO:1000684)
- Orphanet:1656 (MONDO:equivalentTo)
- EFO:1000684 (MONDO:equivalentTo)
- DOID:8505 (MONDO:equivalentTo)
- MEDGEN:8327 (MONDO:equivalentTo)
- GARD:10075 (MONDO:GARD)
- SCTID:111196000 (MONDO:equivalentTo)
- NCIT:C26742 (MONDO:equivalentTo)
- ICD9:694.0 (MONDO:i2s)
ordo_disorder, gard_rare, otar, rare, orphanet_rare
http://linkedlifedata.com/resource/umls/id/C0011608
http://www.orpha.net/ORDO/Orphanet_1656
http://identifiers.org/mesh/D003874
http://purl.obolibrary.org/obo/DOID_8505
http://purl.obolibrary.org/obo/NCIT_C26742
http://identifiers.org/snomedct/111196000
http://purl.bioontology.org/ontology/ICD10CM/L13.0
http://identifiers.org/medgen/8327