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Kasabach-Merritt syndrome

Go to external page http://purl.obolibrary.org/obo/MONDO_0007708

Kasabach-Merritt syndrome (KMS), also known as hemangioma-thrombocytopenia syndrome, is a rare disorder characterized by profound thrombocytopenia, microangiopathic hemolytic anemia, and subsequent consumptive coagulopathy in association with vascular tumors, particularly kaposiform hemangioendothelioma or tufted angioma. [ Orphanet:2330 ]

Synonyms: hemangiomatosis with thrombocytopenia Kasabach Merritt syndrome Kasabach-Merritt Phenomenon thrombocytopenia-hemangioma syndrome Kasabach Merritt phenomenon hemangioma-thrombocytopenia syndrome hemangioma-hemorrhage syndrome Kasabach-Merritt syndrome thrombopenia-hemangioma syndrome

This is just here as a test because I lose it

Term information

database cross reference
  • NORD:1320 (MONDO:NORD)
  • SCTID:86635005 (MONDO:equivalentTo)
  • MESH:D059885 (MONDO:equivalentTo)
  • Orphanet:2330 (OMIM:141000)
  • NANDO:2100297 (https://orcid.org/0000-0003-0011-764X)
  • GARD:70 (MONDO:GARD)
  • NANDO:2201035 (https://orcid.org/0000-0003-0011-764X)
  • UMLS:C0221025 (MONDO:equivalentTo)
  • NCIT:C3821 (MONDO:equivalentTo)
  • ICD9:287.39 (MONDO:relatedTo)
  • MedDRA:10058423 (Orphanet:2330/e)
  • MEDGEN:65122 (MONDO:equivalentTo)
  • OMIM:141000 (Orphanet:2330/e)
Subsets

gard_rare, ordo_disorder, rare, ordo_clinical_situation, nord_rare, orphanet_rare

closeMatch

http://identifiers.org/meddra/10058423

exactMatch

http://identifiers.org/medgen/65122

http://linkedlifedata.com/resource/umls/id/C0221025

https://omim.org/entry/141000

http://purl.obolibrary.org/obo/NCIT_C3821

http://identifiers.org/mesh/D059885

http://identifiers.org/snomedct/86635005

http://www.orpha.net/ORDO/Orphanet_2330

has related synonym

hemangioma thrombocytopenia syndrome

KMP

id

MONDO:0007708

Term relations

Subclass of: