Pemphigus is a group of rare autoimmune diseases that cause blistering of the skin and mucous membranes (mouth, nose, throat, eyes, and genitals).This conditioncan occur at any age, but often strikes people in middle or older age. Studies have shown that some populations may be at greater risk for certain types of pemphigus. For instance, people of Jewish descent and those from India, Southeast Europe, and the Middle East are at greater risk for pemphigus vulargis, while pemphigus foliaceus is more common in North America, Turkey, and South America. Pemphigus is a chronic disease which is best controlled by early diagnosis and treatment.Treatment includes steroids to reduce inflammation,drugs that suppress the immune system responseand antibiotics to treat associated infections. There are four main types of pemphigus: Pemphigus vulgaris Pemphigus foliaceus IgA pemphigus Paraneoplastic pemphigus [ https://rarediseases.info.nih.gov/diseases/7352/pemphigus ]
Term information
- SCTID:65172003 (MONDO:equivalentTo)
- DOID:9182 (MONDO:equivalentTo)
- NANDO:1200228 (https://orcid.org/0000-0003-0011-764X)
- NCIT:C34909 (MONDO:equivalentTo)
- Wikipedia:Pemphigus (EFO:1000749)
- UMLS:C0030807 (MONDO:equivalentTo)
- MESH:D010392 (MONDO:equivalentTo)
- ICD9:694.4 (MONDO:i2s)
- EFO:1000749 (MONDO:equivalentTo)
- MEDGEN:45369 (MONDO:equivalentTo)
- GARD:7352 (MONDO:GARD)
- ICD10CM:L10 (MONDO:equivalentTo)
gard_rare, otar, rare, nord_rare
http://identifiers.org/mesh/D010392
http://purl.obolibrary.org/obo/DOID_9182
http://identifiers.org/medgen/45369
http://purl.bioontology.org/ontology/ICD10CM/L10
http://identifiers.org/snomedct/65172003
http://linkedlifedata.com/resource/umls/id/C0030807
http://purl.obolibrary.org/obo/NCIT_C34909