Developmental syndromes caused by germline mutations (or in rare cases by somatic mosaicism) in genes that alter the Ras subfamily and mitogen-activated protein kinases that control signal transduction. [ http://en.wikipedia.org/wiki/RASopathy ]

Synonyms: disorder of Ras protein signal transduction RASopathy Ras protein signal transduction disease

This is just here as a test because I lose it

Term information

database cross reference
  • GARD:22213 (MONDO:GARD)
  • EFO:1001502 (MONDO:equivalentTo)
  • Orphanet:536391 (https://github.com/monarch-initiative/mondo/issues/606)
  • NCIT:C179667 (MONDO:equivalentTo)
  • DOID:0080690 (MONDO:equivalentTo)
  • MEDGEN:1792298 (MONDO:equivalentTo)
  • UMLS:C5555857 (MONDO:equivalentTo)
Subsets

matrix_llm__is_cancer_other, gard_rare, matrix_llm__is_glucose_dysfunction_other, otar, disease_grouping, matrix_llm__tag_qualy_lost_other, matrix_llm__txgnn_other, matrix_llm__medical_specialization_other, mondo_top_grouping_member, mondo_top_grouping_hereditary_disease, matrix_llm__tag_existing_treatment_other, matrix_included, clingen, matrix_txgnn_grouping_other, matrix_llm__anatomical_other, matrix_llm__is_pathogen_caused_other, rare, harrisons_view_member, harrisons_view_hereditary_disease, ordo_group_of_disorders

ClinGen label
RASopathy [ DOID:0080690 Orphanet:536391 NCIT:C179667 ]

conformsTo

http://purl.obolibrary.org/obo/mondo/patterns/basis_in_disruption_of_process.yaml

http://purl.obolibrary.org/obo/mondo/patterns/disrupts_process.yaml

contributor

https://orcid.org/0000-0002-4142-7153

https://orcid.org/0000-0003-2955-4640

curated content resource

https://search.clinicalgenome.org/kb/conditions/MONDO:0021060

exactMatch

http://www.orpha.net/ORDO/Orphanet_536391

http://purl.obolibrary.org/obo/NCIT_C179667

http://linkedlifedata.com/resource/umls/id/C5555857

http://purl.obolibrary.org/obo/DOID_0080690

http://www.ebi.ac.uk/efo/EFO_1001502

http://identifiers.org/medgen/1792298

id

MONDO:0021060