Primary progressive aphasia (PPA) is a neurodegenerative disorder, characterized by a primary dissolution of language, with relative sparing of other mental faculties for at least the first 2 years of illness. PPA is recognized as the language variant in the frontotemporal dementia (FTD) spectrum of disorders. PPA can be classified into 3 subtypes based on specific speech and language features: semantic dementia (SD), progressive non-fluent aphasia (PNFA) and logopenic progressive aphasia (lv-PPA). [ Orphanet:95432 ]
Synonyms: PPA Mesulam syndrome
Term information
- DOID:0081388 (MONDO:equivalentTo)
- NCIT:C85024 (MONDO:equivalentTo)
- MESH:D018888 (Orphanet:95432/e)
- MEDGEN:79466 (MONDO:equivalentTo)
- Orphanet:95432 (MONDO:equivalentTo)
- EFO:0009053 (MONDO:equivalentTo)
- GARD:8541 (MONDO:GARD)
- UMLS:C0282513 (MONDO:equivalentTo)
gard_rare, matrix_llm__is_cancer_other, matrix_llm__is_glucose_dysfunction_other, otar, matrix_excluded, disease_grouping, matrix_llm__tag_qualy_lost_other, matrix_llm__txgnn_other, matrix_llm__medical_specialization_other, mondo_top_grouping_member, matrix_txgnn_grouping_neurodegenerative_disease, matrix_llm__tag_existing_treatment_other, matrix_llm__anatomical_other, matrix_llm__is_pathogen_caused_other, matrix_txgnn_grouping_member, rare, harrisons_view_member, mondo_top_grouping_nervous_system_disorder, ordo_group_of_disorders, harrisons_view_nervous_system_disorder
http://identifiers.org/medgen/79466
http://purl.obolibrary.org/obo/DOID_0081388
http://identifiers.org/mesh/D018888
http://www.ebi.ac.uk/efo/EFO_0009053
http://linkedlifedata.com/resource/umls/id/C0282513
http://www.orpha.net/ORDO/Orphanet_95432
http://purl.obolibrary.org/obo/NCIT_C85024