A benign, partly cystic, epithelial tumor of the sellar region, presumably derived from Rathke pouch epithelium. It affects mainly children and young adults. There are two clinicopathological forms: adamantinomatous craniopharyngioma and papillary craniopharyngioma. The most significant factor associated with recurrence is the extent of surgical resection, with lesions greater than 5 cm in diameter carrying a markedly worse prognosis. (Adapted from WHO) [ NCIT:C2964 ]
Synonyms: Rathke's pouch tumor Rathke's pouch neoplasm Rathke pouch neoplasm craniopharyngioma (WHO grade I) Rathke pouch tumour Rathke's pouch tumour craniopharyngioma (morphologic abnormality) tumour of Rathke's pouch tumor of Rathke's pouch Rathke pouch tumor neoplasm of Rathke's pouch craniopharyngioma, benign
Term information
- MedDRA:10011318 (Orphanet:54595/e)
- NORD:1996 (MONDO:NORD)
- ICDO:9350/1 (NCIT:C2964)
- ICD9:237.0 (MONDO:relatedTo)
- GARD:10486 (MONDO:GARD)
- MEDGEN:41339 (MONDO:equivalentTo)
- SCTID:189179009 (MONDO:equivalentTo)
- MESH:D003397 (Orphanet:54595/e)
- NANDO:2200091 (https://orcid.org/0000-0003-0011-764X)
- NCIT:C2964 (MONDO:equivalentTo)
- Orphanet:54595 (MONDO:equivalentTo)
- EFO:1000209 (MONDO:equivalentTo)
- UMLS:C0010276 (MONDO:equivalentTo)
- DOID:3840 (MONDO:equivalentTo)
gard_rare, matrix_llm__is_cancer_other, ordo_disorder, matrix_txgnn_grouping_cancer_or_benign_tumor, harrisons_view_connective_tissue_disorder, mondo_top_grouping_member, matrix_llm__txgnn_other, matrix_included, nord_rare, mondo_top_grouping_cancer_or_benign_tumor, matrix_txgnn_grouping_member, rare, harrisons_view_musculoskeletal_system_disorder, orphanet_rare, harrisons_view_nervous_system_disorder, matrix_llm__is_glucose_dysfunction_other, otar, matrix_llm__tag_qualy_lost_other, matrix_llm__medical_specialization_other, mondo_top_grouping_musculoskeletal_system_disorder, matrix_llm__tag_existing_treatment_other, matrix_llm__anatomical_other, matrix_llm__is_pathogen_caused_other, harrisons_view_cancer_or_benign_tumor, harrisons_view_member, mondo_top_grouping_nervous_system_disorder, mondo_top_grouping_connective_tissue_disorder
http://identifiers.org/snomedct/189179009
http://www.ebi.ac.uk/efo/EFO_1000209
http://www.orpha.net/ORDO/Orphanet_54595
http://purl.obolibrary.org/obo/NCIT_C2964
http://purl.obolibrary.org/obo/DOID_3840
http://identifiers.org/mesh/D003397
http://identifiers.org/medgen/41339
http://linkedlifedata.com/resource/umls/id/C0010276
cystoma
craniopharyngeal duct tumor
Dysodontogenic epithelial tumour
Dysodontogenic epithelial tumor
craniopharyngeal duct tumour
Adamantinomatous tumor
Adamantinomatous tumour
Term relations
- [X] neoplasm and disease has location some sella turcica and disease arises from alteration in structure some Rathkes pouch epithelium
- [X] central nervous system organ benign neoplasm
- [X] bone benign neoplasm
- [X] sella turcica neoplasm
- [X] squamous cell neoplasm
- [X] benign epithelial neoplasm
- [X] disorder of facial skeleton
- disease arises from alteration in structure some Rathkes pouch epithelium
- has characteristic some tumor grade 1, general grading system
- disease has location some sella turcica