Langerhans cell histiocytosis (LCH) is a systemic disease associated with the proliferation and accumulation (usually in granulomas) of Langerhans cells in various tissues. [ Orphanet:389 ]
Synonyms: letterer-Siwe disease of spleen letterer-Siwe disease of lymph nodes of head, face and/or neck letterer-Siwe disease of lymph nodes of inguinal region and/or lower limb letterer-Siwe disease of intrathoracic lymph nodes letterer-Siwe disease involving lymph nodes of inguinal region and lower limb letterer-Siwe disease of lymph nodes of inguinal region and lower limb letterer-Siwe disease involving lymph nodes of multiple sites Langerhan's cell histiocytosis letterer-Siwe disease of intra-abdominal lymph nodes Langerhans cell granulomatosis letterer-Siwe disease involving intra-abdominal lymph nodes letterer-Siwe disease involving spleen letterer-Siwe disease involving lymph nodes of axilla and upper limb letterer-Siwe disease of lymph nodes of axilla and upper limb Langerhans cell histiocytosis letterer-Siwe disease of intrapelvic lymph nodes letterer-Siwe disease of lymph nodes of head, face and neck letterer-Siwe disease involving intrathoracic lymph nodes letterer-Siwe disease of lymph nodes of multiple sites letterer-Siwe disease of lymph nodes of axilla and/or upper limb LCH letterer-Siwe disease of lymph nodes of inguinal region amd/or lower limb letterer-Siwe disease involving lymph nodes of head, face and neck letterer-Siwe disease involving lymph nodes of head, face, and neck Langerhans cell histiocytosis, Not otherwise specified letterer-Siwe disease involving intrapelvic lymph nodes histiocytosis X Langerhans cell histiocytosis, NOS
Term information
- ICDO:9754/3 (NCIT:C3107)
- SCTID:65399007 (MONDO:equivalentTo)
- icd11.foundation:1388720498 (MONDO:equivalentTo)
- GARD:6858 (MONDO:GARD)
- NANDO:2200031 (https://orcid.org/0000-0003-0011-764X)
- NORD:1348 (MONDO:NORD)
- ICDO:9752/1 (NCIT:C3107)
- EFO:1000318 (MONDO:equivalentTo)
- ICDO:9751/1 (NCIT:C3107)
- icd11.foundation:216625985 (Orphanet:389)
- ICD9:277.89 (MONDO:relatedTo)
- ICDO:9753/1 (NCIT:C3107)
- NCIT:C3107 (MONDO:equivalentTo)
- UMLS:C0019621 (MONDO:equivalentTo)
- ONCOTREE:LCH (MONDO:equivalentTo)
- MedDRA:10069698 (Orphanet:389/e)
- Orphanet:389 (OMIM:604856)
- MEDGEN:5568 (MONDO:equivalentTo)
- DOID:2571 (MONDO:equivalentTo)
- OMIM:604856 (Orphanet:389/e)
- ICD9:202.5 (DOID:2571)
- ICDO:9751/3 (NCIT:C3107)
matrix_llm__is_cancer_other, ordo_disorder, gard_rare, matrix_txgnn_grouping_cancer_or_benign_tumor, disease_grouping, matrix_llm__txgnn_other, mondo_top_grouping_member, harrisons_view_immune_system_disorder, matrix_included, nord_rare, mondo_top_grouping_cancer_or_benign_tumor, matrix_txgnn_grouping_member, mondo_top_grouping_immune_system_disorder, rare, orphanet_rare, matrix_llm__is_glucose_dysfunction_other, otar, matrix_llm__tag_qualy_lost_other, mondo_top_grouping_hematologic_disorder, matrix_llm__medical_specialization_other, matrix_llm__tag_existing_treatment_other, matrix_llm__anatomical_other, matrix_llm__is_pathogen_caused_other, harrisons_view_hematologic_disorder, harrisons_view_cancer_or_benign_tumor, harrisons_view_member
http://purl.obolibrary.org/obo/mondo/sources/icd11foundation/1388720498
http://www.ebi.ac.uk/efo/EFO_1000318
http://identifiers.org/snomedct/65399007
http://www.orpha.net/ORDO/Orphanet_389
https://omim.org/entry/604856
http://purl.obolibrary.org/obo/mondo/sources/icd11foundation/216625985
http://purl.obolibrary.org/obo/NCIT_C3107
http://purl.obolibrary.org/obo/DOID_2571
http://identifiers.org/medgen/5568
http://linkedlifedata.com/resource/umls/id/C0019621