Frontotemporal dementia (FTD) comprises a group of neurodegenerative disorders, characterized by progressive changes in behavior, executive dysfunction and language impairment, as a result of degeneration of the medial prefrontal and frontoinsular cortices. Four clinical subtypes have been identified: semantic dementia, progressive non-fluent aphasia, behavioral variant FTD and right temporal lobar atrophy. [ Orphanet:282 ]
Synonyms: Wilhemsen-Lynch disease multiple system tauopathy with presenile dementia pallidopontonigral degeneration FTD frontotemporal lobar degeneration
Term information
- icd11.foundation:831337417 (Orphanet:282)
- MedDRA:10068968 (Orphanet:282/e)
- GARD:8436 (MONDO:GARD)
- MESH:D057180 (Orphanet:282/e)
- Orphanet:282 (MONDO:equivalentTo)
- DOID:9255 (MONDO:equivalentTo)
- NCIT:C84719 (MONDO:equivalentTo)
- MEDGEN:83266 (MONDO:equivalentTo)
- NANDO:1200548 (https://orcid.org/0000-0003-0011-764X)
- UMLS:C0338451 (MONDO:equivalentTo)
gard_rare, matrix_llm__is_cancer_other, disease_grouping, mondo_top_grouping_member, matrix_llm__txgnn_other, harrisons_view_psychiatric_disorder, matrix_included, matrix_txgnn_grouping_member, rare, matrix_txgnn_grouping_psychiatric_disorder, harrisons_view_nervous_system_disorder, matrix_llm__is_glucose_dysfunction_other, otar, matrix_llm__tag_qualy_lost_other, matrix_llm__medical_specialization_other, mondo_top_grouping_hereditary_disease, matrix_txgnn_grouping_neurodegenerative_disease, matrix_llm__tag_existing_treatment_other, mondo_top_grouping_psychiatric_disorder, matrix_llm__anatomical_other, matrix_llm__is_pathogen_caused_other, harrisons_view_member, mondo_top_grouping_nervous_system_disorder, harrisons_view_hereditary_disease, ordo_group_of_disorders
http://purl.obolibrary.org/obo/NCIT_C84719
http://identifiers.org/mesh/D057180
http://identifiers.org/medgen/83266
http://linkedlifedata.com/resource/umls/id/C0338451
http://www.orpha.net/ORDO/Orphanet_282
http://purl.obolibrary.org/obo/mondo/sources/icd11foundation/831337417
http://purl.obolibrary.org/obo/DOID_9255