An autosomal recessive disorder caused by mutation(s) in the TUBGCP6 gene, encoding gamma-tubulin complex component 6. It is characterized by microcephaly and chorioretinopathy. [ NCIT:C129306 ]

Synonyms: microcephaly and chorioretinopathy caused by mutation in TUBGCP6 microcephaly and chorioretinopathy, autosomal recessive, type 1 TUBGCP6 microcephaly and chorioretinopathy Pseudotoxoplasmosis syndrome microcephaly and chorioretinopathy 1 autosomal recessive chorioretinopathy-microcephaly-intellectual disability syndrome microcephaly and chorioretinopathy type 1

This is just here as a test because I lose it

Term information

database cross reference
  • OMIM:251270 (Orphanet:2518/e)
  • DOID:0080105 (MONDO:equivalentTo)
  • Orphanet:2518 (OMIM:251270)
  • UMLS:C3278481 (MONDO:equivalentTo)
  • NCIT:C129306 (MONDO:equivalentTo)
  • MEDGEN:480111 (MONDO:equivalentTo)
  • GARD:16603 (MONDO:GARD)
Subsets

matrix_llm__is_cancer_other, ordo_disorder, gard_rare, mondo_top_grouping_disorder_of_visual_system, matrix_llm__txgnn_other, mondo_top_grouping_member, harrisons_view_psychiatric_disorder, matrix_included, nord_rare, clingen, harrisons_view_inflammatory_disease, matrix_txgnn_grouping_member, rare, mondo_top_grouping_inflammatory_disease, matrix_txgnn_grouping_psychiatric_disorder, orphanet_rare, harrisons_view_nervous_system_disorder, mondo_top_grouping_syndromic_disease, matrix_llm__is_glucose_dysfunction_other, otar, harrisons_view_disorder_of_development_or_morphogenesis, matrix_llm__tag_qualy_lost_other, matrix_llm__medical_specialization_other, mondo_top_grouping_hereditary_disease, harrisons_view_disorder_of_visual_system, matrix_llm__tag_existing_treatment_other, mondo_top_grouping_psychiatric_disorder, matrix_llm__anatomical_other, matrix_llm__is_pathogen_caused_other, harrisons_view_member, ordo_malformation_syndrome, mondo_top_grouping_nervous_system_disorder, harrisons_view_syndromic_disease, harrisons_view_hereditary_disease, mondo_top_grouping_disorder_of_development_or_morphogenesis, mondo_top_grouping_disorder_of_orbital_region

ClinGen label
microcephaly and chorioretinopathy 1 [ DOID:0080105 ]

abbreviation
MCCRP1 [ MONDO:Lexical ]

curated content resource

https://search.clinicalgenome.org/kb/conditions/MONDO:0009624

exactMatch

http://www.orpha.net/ORDO/Orphanet_2518

https://omim.org/entry/251270

http://identifiers.org/medgen/480111

http://purl.obolibrary.org/obo/DOID_0080105

http://purl.obolibrary.org/obo/NCIT_C129306

http://linkedlifedata.com/resource/umls/id/C3278481

excluded subClassOf

http://purl.obolibrary.org/obo/MONDO_0015368

has related synonym

MCCRP1

microcephaly and chorioretinopathy, autosomal recessive, 1

autosomal recessive chorioretinopathy-microcephaly syndrome

id

MONDO:0009624

term tracker item

https://github.com/monarch-initiative/mondo/pull/2571/