A chronic, relapsing, multisystemic vasculitis characterized by mucocutaneous lesions, as well as articular, vascular, ocular and central nervous system manifestations. [ Orphanet:117 ]
Synonyms: Behcet's syndrome Behçet's syndrome Morbus Behçet's syndrome Behçet disease Behçet-Adamantiades syndrome silk road disease Bechet syndrome triple symptom complex Behçet syndrome Behet's syndrome Behcet syndrome Adamantiades-Behcet disease Behcet disease
Term information
- MEDGEN:2568 (MONDO:equivalentTo)
- Orphanet:117 (OMIM:109650)
- NANDO:1200284 (https://orcid.org/0000-0003-0011-764X)
- NCIT:C34416 (MONDO:equivalentTo)
- OMIM:109650 (Orphanet:117/e)
- GARD:848 (MONDO:GARD)
- EFO:0003780 (MONDO:equivalentTo)
- SCTID:310701003 (MONDO:equivalentTo)
- MedDRA:10004213 (Orphanet:117/e)
- ICD9:136.1 (MONDO:i2s)
- UMLS:C0004943 (MONDO:equivalentTo)
- icd11.foundation:1668927157 (https://orcid.org/0000-0002-4142-7153)
- NANDO:2200422 (https://orcid.org/0000-0003-0011-764X)
- MESH:D001528 (Orphanet:117/e)
- DOID:13241 (MONDO:equivalentTo)
matrix_llm__is_cancer_other, ordo_disorder, gard_rare, matrix_llm__is_glucose_dysfunction_other, otar, matrix_llm__tag_qualy_lost_other, mondo_top_grouping_integumentary_system_disorder, matrix_llm__medical_specialization_other, matrix_llm__txgnn_other, mondo_top_grouping_member, matrix_txgnn_grouping_cardiovascular_disorder, matrix_llm__tag_existing_treatment_other, matrix_included, matrix_llm__anatomical_other, matrix_llm__is_pathogen_caused_other, harrisons_view_cardiovascular_disorder, matrix_txgnn_grouping_member, rare, harrisons_view_member, mondo_top_grouping_cardiovascular_disorder, harrisons_view_syndromic_disease, orphanet_rare, mondo_top_grouping_syndromic_disease, harrisons_view_integumentary_system_disorder
http://linkedlifedata.com/resource/umls/id/C0004943
http://purl.obolibrary.org/obo/DOID_13241
http://purl.obolibrary.org/obo/NCIT_C34416
http://www.orpha.net/ORDO/Orphanet_117
http://purl.obolibrary.org/obo/mondo/sources/icd11foundation/1668927157
https://omim.org/entry/109650
http://identifiers.org/mesh/D001528
http://www.ebi.ac.uk/efo/EFO_0003780
http://identifiers.org/snomedct/310701003
http://identifiers.org/medgen/2568
http://purl.obolibrary.org/obo/MONDO_0017957
http://purl.obolibrary.org/obo/MONDO_0017260
http://purl.obolibrary.org/obo/MONDO_0017370
http://purl.obolibrary.org/obo/MONDO_0015488
http://purl.obolibrary.org/obo/MONDO_0017261
http://purl.obolibrary.org/obo/MONDO_0019724
http://purl.obolibrary.org/obo/MONDO_0017259
http://purl.obolibrary.org/obo/MONDO_0015657
Term relations
- [X] syndromic disease
- [X] skin vascular disease
- disease has location some blood vessel
- disease has feature some Uveitis