An adenocarcinoma arising from the pancreas. It is characterized by the presence of relatively uniform malignant cells which form acinar patterns. It usually occurs during adulthood. Signs and symptoms include abdominal pain, weight loss, nausea, and diarrhea. It may metastasize to regional lymph nodes and the liver. A minority of patients develop lipase hypersecretion syndrome. This syndrome may be seen in patients with liver metastases and it is characterized by excessive secretion of lipase in the serum, polyarthralgia, and subcutaneous fat necrosis. [ NCIT:C7977 ]
Synonyms: Pancreatic acinar cell cancer acinar cell adenocarcinoma of the pancreas pancreas acinar cell adenocarcinoma carcinoma of pancreatic acinar cell acinar cell adenocarcinoma of pancreas pancreatic acinar cell adenocarcinoma acinar cell carcinoma of pancreas pancreatic acinar cell carcinoma acinar cell carcinoma of the pancreas
Term information
- UMLS:C0279661 (MONDO:equivalentTo)
- NCIT:C7977 (MONDO:equivalentTo)
- Orphanet:424046 (MONDO:equivalentTo)
- EFO:1000439 (MONDO:equivalentTo)
- GARD:21777 (MONDO:GARD)
- ONCOTREE:PAAC (MONDO:equivalentTo)
- MEDGEN:83540 (MONDO:equivalentTo)
- DOID:5742 (MONDO:equivalentTo)
ordo_disorder, gard_rare, matrix_llm__is_cancer_other, matrix_txgnn_grouping_cancer_or_benign_tumor, harrisons_view_endocrine_system_disorder, matrix_llm__txgnn_other, mondo_top_grouping_member, matrix_txgnn_grouping_endocrine_system_disorder, matrix_included, nord_rare, mondo_top_grouping_cancer_or_benign_tumor, matrix_txgnn_grouping_member, rare, orphanet_rare, mondo_top_grouping_digestive_system_disorder, matrix_llm__is_glucose_dysfunction_other, otar, matrix_llm__tag_qualy_lost_other, matrix_llm__medical_specialization_other, mondo_top_grouping_endocrine_system_disorder, matrix_llm__tag_existing_treatment_other, matrix_llm__anatomical_other, harrisons_view_digestive_system_disorder, matrix_llm__is_pathogen_caused_other, harrisons_view_cancer_or_benign_tumor, harrisons_view_member
http://www.ebi.ac.uk/efo/EFO_1000439
http://purl.obolibrary.org/obo/DOID_5742
http://purl.obolibrary.org/obo/NCIT_C7977
http://identifiers.org/medgen/83540
http://linkedlifedata.com/resource/umls/id/C0279661
http://www.orpha.net/ORDO/Orphanet_424046