A benign or malignant neoplasm arising from paraganglia located along the sympathetic or parasympathetic nerves. Infrequently, it may arise outside the usual distribution of the sympathetic and parasympathetic paraganglia. Tumors arising from the adrenal gland medulla are called pheochromocytomas. Morphologically, paragangliomas usually display a nesting (Zellballen) growth pattern. There are no reliable morphologic criteria to distinguish between benign and malignant paragangliomas. The only definitive indicator of malignancy is the presence of regional or distant metastases. [ NCIT:C3308 ]
Synonyms: neoplasm of paraganglion neoplasm of the paraganglion tumor of the paraganglion tumor of paraganglion paraganglion tumour paraganglion tumor paraganglioma Paraganglionic tumour tumour of the paraganglion paraganglion neoplasm paragangliomas Paraganglionic neoplasm tumour of paraganglion Paraganglionic tumor
Term information
- SCTID:127027008 (MONDO:equivalentTo)
- DOID:0050773 (MONDO:equivalentTo)
- MESH:D010235 (MONDO:equivalentTo)
- ONCOTREE:PGNG (MONDO:equivalentTo)
- OMIMPS:168000 (https://orcid.org/0000-0002-6601-2165)
- ICDO:8680/1 (NCIT:C3308)
- EFO:1000453 (MONDO:equivalentTo)
- NCIT:C3308 (MONDO:equivalentTo)
- UMLS:C0030421 (MONDO:equivalentTo)
- ICD9:239.7 (MONDO:relatedTo)
- MEDGEN:10571 (MONDO:equivalentTo)
gard_rare, matrix_llm__is_cancer_other, matrix_txgnn_grouping_cancer_or_benign_tumor, matrix_llm__txgnn_other, harrisons_view_endocrine_system_disorder, mondo_top_grouping_member, matrix_txgnn_grouping_endocrine_system_disorder, mondo_top_grouping_cancer_or_benign_tumor, matrix_txgnn_grouping_member, rare, harrisons_view_nervous_system_disorder, matrix_llm__is_glucose_dysfunction_other, otar, matrix_excluded, harrisons_view_disorder_of_development_or_morphogenesis, matrix_llm__tag_qualy_lost_other, matrix_llm__medical_specialization_other, mondo_top_grouping_endocrine_system_disorder, mondo_top_grouping_hereditary_disease, matrix_llm__tag_existing_treatment_other, matrix_llm__anatomical_other, matrix_llm__is_pathogen_caused_other, harrisons_view_cancer_or_benign_tumor, harrisons_view_member, mondo_top_grouping_nervous_system_disorder, harrisons_view_hereditary_disease, mondo_top_grouping_disorder_of_development_or_morphogenesis
http://identifiers.org/snomedct/127027008
https://omim.org/phenotypicSeries/PS168000
http://identifiers.org/medgen/10571
http://www.ebi.ac.uk/efo/EFO_1000453
http://identifiers.org/mesh/D010235
http://purl.obolibrary.org/obo/DOID_0050773
http://purl.obolibrary.org/obo/NCIT_C3308
http://linkedlifedata.com/resource/umls/id/C0030421
Term relations
- [X] neuroendocrine neoplasm and disease has location some autonomic nervous system and disease arises from alteration in structure some neural crest cell