A benign or malignant neoplasm arising from paraganglia located along the sympathetic or parasympathetic nerves. Infrequently, it may arise outside the usual distribution of the sympathetic and parasympathetic paraganglia. Tumors arising from the adrenal gland medulla are called pheochromocytomas. Morphologically, paragangliomas usually display a nesting (Zellballen) growth pattern. There are no reliable morphologic criteria to distinguish between benign and malignant paragangliomas. The only definitive indicator of malignancy is the presence of regional or distant metastases. [ NCIT:C3308 ]

Synonyms: neoplasm of paraganglion neoplasm of the paraganglion tumor of the paraganglion tumor of paraganglion paraganglion tumour paraganglion tumor paraganglioma Paraganglionic tumour tumour of the paraganglion paraganglion neoplasm paragangliomas Paraganglionic neoplasm tumour of paraganglion Paraganglionic tumor

This is just here as a test because I lose it

Term information

database cross reference
  • SCTID:127027008 (MONDO:equivalentTo)
  • DOID:0050773 (MONDO:equivalentTo)
  • MESH:D010235 (MONDO:equivalentTo)
  • ONCOTREE:PGNG (MONDO:equivalentTo)
  • OMIMPS:168000 (https://orcid.org/0000-0002-6601-2165)
  • ICDO:8680/1 (NCIT:C3308)
  • EFO:1000453 (MONDO:equivalentTo)
  • NCIT:C3308 (MONDO:equivalentTo)
  • UMLS:C0030421 (MONDO:equivalentTo)
  • ICD9:239.7 (MONDO:relatedTo)
  • MEDGEN:10571 (MONDO:equivalentTo)
Subsets

gard_rare, matrix_llm__is_cancer_other, matrix_txgnn_grouping_cancer_or_benign_tumor, matrix_llm__txgnn_other, harrisons_view_endocrine_system_disorder, mondo_top_grouping_member, matrix_txgnn_grouping_endocrine_system_disorder, mondo_top_grouping_cancer_or_benign_tumor, matrix_txgnn_grouping_member, rare, harrisons_view_nervous_system_disorder, matrix_llm__is_glucose_dysfunction_other, otar, matrix_excluded, harrisons_view_disorder_of_development_or_morphogenesis, matrix_llm__tag_qualy_lost_other, matrix_llm__medical_specialization_other, mondo_top_grouping_endocrine_system_disorder, mondo_top_grouping_hereditary_disease, matrix_llm__tag_existing_treatment_other, matrix_llm__anatomical_other, matrix_llm__is_pathogen_caused_other, harrisons_view_cancer_or_benign_tumor, harrisons_view_member, mondo_top_grouping_nervous_system_disorder, harrisons_view_hereditary_disease, mondo_top_grouping_disorder_of_development_or_morphogenesis

ClinGen label
paraganglioma [ NCIT:C3308 DOID:0050773 ]

UK spelling synonym
tumour of paraganglion

UK spelling synonym
Paraganglionic tumour

UK spelling synonym
paraganglion tumour

UK spelling synonym
tumour of the paraganglion

exactMatch

http://identifiers.org/snomedct/127027008

https://omim.org/phenotypicSeries/PS168000

http://identifiers.org/medgen/10571

http://www.ebi.ac.uk/efo/EFO_1000453

http://identifiers.org/mesh/D010235

http://purl.obolibrary.org/obo/DOID_0050773

http://purl.obolibrary.org/obo/NCIT_C3308

http://linkedlifedata.com/resource/umls/id/C0030421

has narrow synonym

chemodectoma

id

MONDO:0000448

should conform to

http://purl.obolibrary.org/obo/mondo/patterns/OMIM_phenotypic_series.yaml

term tracker item

https://github.com/monarch-initiative/mondo/issues/6877