phagocytic cell dysfunction
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MONDO_0024627 |
|
defective phagocytic cell engulfment
|
MONDO_0024626 |
|
epidermal disease
|
MONDO_0019268 |
[A skin disease that involves the epidermis.] |
hair anomaly
|
MONDO_0019278 |
|
integumentary system disorder
|
MONDO_0002051 |
[A disease involving the integumental system.] |
erythrokeratoderma
|
MONDO_0019270 |
[An umbrella term for a group of rare genetic skin disorders characterized by well-demarcated plaques of reddened, dry and thickened skin. Typically, these lesions are distributed symmetrically on the body and tend to slowly expand and progress over time.] |
bilateral polymicrogyria
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MONDO_0017091 |
[Bilateral polymicrogyria is a rare cerebral malformation due to abnormal neuronal migration defined as a cerebral cortex with many excessively small convolutions. It presents with developmental delay, intellectual disability, seizures and various neurological impairments and may be isolated or comprise a clinical feature of many genetic syndromes. It may also be associated with perinatal cytomegalovirus infection.] |
polymicrogyria
|
MONDO_0000087 |
[A developmental brain abnormality characterized by an excessive amount of small convolutions on the surface of the brain and cognitive dysfunction.] |
amyotrophic lateral sclerosis type 15
|
MONDO_0010459 |
[Any amyotrophic lateral sclerosis in which the cause of the disease is a mutation in the UBQLN2 gene.] |
familial meningioma
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MONDO_0011789 |
[A meningioma that is transmitted from the parents to an offspring.] |
osteogenesis imperfecta type 2
|
MONDO_0008147 |
[Osteogenesis imperfecta type II is a lethal type of osteogenesis imperfecta (OI), a genetic disorder characterized by increased bone fragility, low bone mass and susceptibility to bone fractures. Patients with type II present multiple rib and long bone fractures at birth, marked deformities, broad long bones, low density on skull X-rays, and dark sclera.] |
osteogenesis imperfecta and a reduction of bone mineral density.
|
MONDO_0800064 |
[A skeletal dysplasia characterized by osteogenesis imperfecta and decreased bone density.] |
variable age onset epilepsy
|
MONDO_0100036 |
[An epilepsy syndrome that has an onset during variable ages and stages of life.] |
osteogenesis imperfecta type 4
|
MONDO_0008148 |
[Osteogenesis imperfecta type IV is a moderate type of osteogenesis imperfecta (OI), a genetic disorder characterized by increased bone fragility, low bone mass and susceptibility to bone fractures. Patients with type IV have moderately short stature, mild to moderate scoliosis, grayish or white sclera, and dentinogenesis imperfecta (DI).] |
combined immunodeficiency due to DOCK8 deficiency
|
MONDO_0009478 |
[Combined immunodeficiency due to dedicator of cytokinesis 8 protein (DOCK8) deficiency is a form of T and B cell immunodeficiency characterized by recurrent cutaneous viral infections, susceptibility to cancer and elevated serum levels of immunoglobulin E (IgE).] |
porphyrin metabolism disease
|
MONDO_0037821 |
[A disease that has its basis in the disruption of porphyrin-containing compound metabolic process.] |
spinocerebellar ataxia type 29
|
MONDO_0007298 |
[Spinocerebellar ataxia type 29 (SCA29) is a rare subtype of autosomal dominant cerebellar ataxia type I (ADCA type I) characterized by very slowly progressive or non-progressive ataxia, dysarthria, oculomotor abnormalities and intellectual disability.] |
autosomal dominant cerebellar ataxia type I
|
MONDO_0019792 |
[Autosomal dominant cerebellar ataxia (ADCA) type I is a group of spinocerebellar ataxias (SCAs) characterized by ataxia with other neurological signs, including oculomotor disturbances, cognitive deficits, pyramidal and extrapyramidal dysfunction, bulbar, spinal and peripheral nervous system involvement.] |
osteogenesis imperfecta type 1
|
MONDO_0008146 |
[Osteogenesis imperfecta type I is a mild type of osteogenesis imperfecta (OI), a genetic disorder characterized by increased bone fragility, low bone mass and susceptibility to bone fractures.] |
CDKL5 disorder
|
MONDO_0100039 |
[A monogenic disease that has material basis in mutation in the CDKL5 gene.] |