hyper-IgE recurrent infection syndrome 1, autosomal dominant
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MONDO_0007818 |
[A condition of decreased or absent presence or activity of signal transducer and activator of transcription 3 protein. Deficiency of this protein is associated with hyper-IgE syndrome.] |
hyper-IgE syndrome
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MONDO_0018037 |
[A condition that is characterized by elevated serum IgE, dermatitis, and respiratory infections.] |
inclusion body myositis
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MONDO_0007827 |
[A slowly progressive degenerative inflammatory disorder of skeletal muscles characterized by late onset weakness of specific muscles and distinctive histopathological features.] |
myositis disease
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MONDO_0021167 |
[An inflammatory disease involving a pathogenic inflammatory response in the muscle tissue.] |
optic nerve disorder
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MONDO_0002135 |
[A non-neoplastic or neoplastic disorder affecting the optic nerve (second cranial nerve).] |
cranial nerve neuropathy
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MONDO_0003569 |
[A neoplastic or non-neoplastic disorder that affects one of the cranial nerves.] |
central nervous system disorder
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MONDO_0002602 |
[A disease involving the central nervous system.] |
disorder of visual system
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MONDO_0024458 |
[A disease that involves the visual system.] |
NKX2-1 related choreoathetosis and congenital hypothyroidism with or without pulmonary dysfunction
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MONDO_0100520 |
[The NKX2-1 gene is located on chromosome 14 at 14q13.3 and encodes the NK2 homeobox 1 protein, a transcription factor that binds and activates thyroid specific genes. NKX2-1 was first reported in relation to autosomal dominant NKX2-1 related choreoathetosis and congenital hypothyroidism with or without pulmonary dysfunction in 1998.] |
Alport syndrome
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MONDO_0018965 |
[A rare renal disease characterized by glomerular nephropathy with hematuria progressing to end-stage renal disease (ESRD), frequently associated with sensorineural deafness, and occasionally with ocular anomalies.] |
hereditary nephritis
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MONDO_0005334 |
[A group of inherited conditions characterized initially by hematuria and slowly progressing to renal insufficiency. The most common form is the Alport syndrome (hereditary nephritis with hearing loss) which is caused by mutations in genes for type IV collagen and defective glomerular basement membrane.] |
homocystinuria without methylmalonic aciduria
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MONDO_0018964 |
[Homocystinuria without methylmalonic aciduria is an inborn error of vitamin B12 (cobalamin) metabolism characterized by megaloblastic anemia, encephalopathy and, sometimes, developmental delay, and associated with homocystinuria and hyperhomocysteinemia. There are three types of homocystinuria without methylmalonic aciduria; cblE, cblG and cblD-variant 1 (cblDv1).] |
inherited deficiency anemia
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MONDO_0016624 |
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inborn disorder of cobalamin metabolism and transport
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MONDO_0019220 |
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pyruvate metabolism disorder
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MONDO_0016789 |
[An inherited metabolic disease that is has its basis in the disruption of pyruvate metabolic process.] |
inborn disorder of energy metabolism
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MONDO_0019243 |
[An inherited metabolic disease that is has its basis in the disruption of generation of precursor metabolites and energy.] |
TCF12-related craniosynostosis
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MONDO_0014128 |
[Any syndromic craniosynostosis in which the cause of the disease is a mutation in the TCF12 gene.] |
frontonasal dysplasia - severe microphthalmia - severe facial clefting syndrome
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MONDO_0013271 |
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frontonasal dysplasia
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MONDO_0016643 |
[A group of rare bone development disorders characterized by an array of abnormalities affecting the eyes, forehead, and nose, and linked to midfacial dysraphia. The clinical picture is highly variable, but the major findings include hypertelorism, a broad nasal root, a large and bifid nasal tip, and widow's peak. Occasionally, abnormalities can include accessory nasal tags, cleft lip, ocular abnormalities (coloboma, cataract, microphthalmia), conductive hearing loss, basal encephalocele and/or agenesis of the corpus callosum. Intellectual deficit is rare and more likely to occur in cases where hypertelorism is severe or where there is extra-cranial involvement.] |
Charcot-Marie-Tooth disease type 2D
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MONDO_0011091 |
[Autosomal dominant Charcot-Marie-Tooth disease type 2D (CMT2D) is a form of axonal Charcot-Marie-Tooth disease, a peripheral sensorimotor neuropathy, characterized by distal weakness primarily and predominantly occurring in the upper limbs and tendon reflexes absent or reduced in the arms and decreased in the legs. Progression is slow.] |