Myopathy caused by pathogenic variants in SELENON that is congenital or present early in childhood with neonatal hypotonia, delayed motor development, axial muscle weakness, scoliosis, and significant respiratory involvement. Spinal rigidity of varying severity is often present. [ http://www.ncbi.nlm.nih.gov/pubmed/12192640 ]

Synonyms: SEPN1-related myopathy SELENON-related myopathy

This is just here as a test because I lose it

Term information

Subsets

rare, inferred_rare, clingen

creator

https://orcid.org/0000-0001-5208-3432

id

MONDO:0100100

seeAlso

https://search.clinicalgenome.org/kb/conditions/MONDO:0100100

Term relations

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