A benign or malignant paraganglioma arising from the chromaffin cells of the paraganglia that are located along the sympathetic nerves. It includes extra-adrenal paragangliomas and paragangliomas that arise from the adrenal medulla. The latter are commonly referred to as pheochromocytomas. Representative examples of extra-adrenal sympathetic paragangliomas include the bladder, and superior and inferior paraaortic paragangliomas. Clinical signs are related to the secretion of catecholamines resulting in hypertension. [ NCIT:C4216 ]
Synonyms: paraganglioma of sympathetic nervous system sympathetic paraganglioma chromaffin tumor Chromaffinoma chromaffin neoplasm chromaffin tumour sympathetic Paraganglionic neoplasm sympathetic nervous system paraganglioma
Term information
- ICDO:8681/1 (NCIT:C4216)
- NCIT:C4216 (MONDO:equivalentTo)
- UMLS:C0334415 (MONDO:equivalentTo)
- MEDGEN:137758 (MONDO:equivalentTo)
- SCTID:399343007 (MONDO:equivalentTo)
- MESH:C531777 (MONDO:equivalentTo)
gard_rare, otar, rare
http://identifiers.org/medgen/137758
http://purl.obolibrary.org/obo/NCIT_C4216
http://identifiers.org/mesh/C531777
http://linkedlifedata.com/resource/umls/id/C0334415
http://identifiers.org/snomedct/399343007