Ewing sarcoma/peripheral primitive neuroectodermal tumor
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A spectrum of malignant tumors, affecting mostly males under age 20, characterized morphologically by the presence of small round cells. Ewing sarcoma and peripheral primitive neuroectodermal tumor represent the ends of a spectrum, with Ewing sarcoma lacking evidence of neural differentiation and the markers that characterize the peripheral primitive neuroectodermal tumor. Ewing sarcoma and peripheral primitive neuroectodermal tumor may share cytogenetic abnormalities, proto-oncogene expression, cell culture and immunohistochemical abnormalities. These tumors may occur in the soft tissues or the bones. Pain and the presence of a mass are the most common clinical symptoms. [ NCIT:C27291 ]
Synonyms: EFTs Ewing sarcoma family of tumours Ewing family of tumours Ewing's family of tumours Ewing's sarcoma/peripheral primitive neuroectodermal tumor Ewing's sarcoma/peripheral primitive neuroectodermal tumour tumors of Ewing's family Ewing sarcoma family of tumors tumours of Ewing's family Ewing family of tumors tumours of the Ewing's family tumors of the Ewing's family Ewing sarcoma/peripheral primitive neuroectodermal tumor Ewing sarcoma/peripheral PNET Ewing's family of tumors
Term information
- MEDGEN:760735 (MONDO:equivalentTo)
- NCIT:C27291 (https://orcid.org/0000-0002-6601-2165)
- UMLS:C3536893 (MONDO:equivalentTo)
otar
http://identifiers.org/medgen/760735
http://linkedlifedata.com/resource/umls/id/C3536893
http://purl.obolibrary.org/obo/NCIT_C27291