Pancreatic endocrine tumor, also known as pancreatic neuroendocrine tumor (PNET), describes a group of endocrine tumors originating in the pancreas that are usually indolent and benign, but may have the potential to be malignant. They can be functional, exhibiting a hormonal hypersecretion syndrome, but can be non-functional presenting with non-specific symptoms and include insulinoma, glucagonoma, VIPoma, somatostatinoma (SSoma), PPoma and Zollinger-Ellison syndrome (ZES, or gastrinoma) and other ectopic hormone producing tumors (such as GRFoma). [ Orphanet:97253 ]
Synonyms: islet cell tumors - pancreas well differentiated pancreatic endocrine neoplasm well-differentiated NEN of pancreas islet cell tumours of the pancreas islet cell tumors of the pancreas well-differentiated pancreatic neuroendocrine neoplasm well differentiated pancreatic endocrine tumor well differentiated pancreatic endocrine tumour well-differentiated neuroendocrine neoplasm of pancreas islet cell tumour pancreatic neuroendocrine tumor well-differentiated pancreatic NEN islet cell tumor islet cell tumours - pancreas pancreatic NET
Term information
- ICDO:8150/1 (NCIT:C27720)
- UMLS:C1337011 (MONDO:equivalentTo)
- GARD:13034 (MONDO:GARD)
- Orphanet:97253 (MONDO:equivalentTo)
- ONCOTREE:PANET (MONDO:equivalentTo)
- EFO:1000045 (MONDO:equivalentTo)
- NCIT:C27720 (MONDO:equivalentTo)
- MEDGEN:277875 (MONDO:equivalentTo)
gard_rare, otar, disease_grouping, rare, ordo_group_of_disorders
http://purl.obolibrary.org/obo/NCIT_C27720
http://identifiers.org/medgen/277875
http://linkedlifedata.com/resource/umls/id/C1337011
http://www.orpha.net/ORDO/Orphanet_97253
neuroendocrine tumour of pancreas
neuroendocrine tumor of pancreas
PANET
pancreatic endocrine tumor
pancreatic endocrine tumour