A neoplastic proliferation of Langerhans cells with overtly malignant cytologic features. It can be considered a higher grade variant of Langerhans cell histiocytosis (LCH) and it can present de novo or progress from antecedent LCH. (WHO, 2001) [ NCIT:C6921 ]
Synonyms: Langerhans cell sarcoma sarcoma of Langerhans cell
Term information
- SCTID:724649000 (MONDO:equivalentTo)
- ONCOTREE:LCS (MONDO:equivalentTo)
- MEDGEN:266041 (MONDO:equivalentTo)
- NCIT:C6921 (MONDO:exact-label-match)
- MESH:D054752 (Orphanet:86897/e)
- Orphanet:86897 (MONDO:equivalentTo)
- GARD:10491 (MONDO:GARD)
- ICDO:9756/3 (NCIT:C6921)
- NANDO:2200036 (https://orcid.org/0000-0003-0011-764X)
- icd11.foundation:588958190 (Orphanet:86897)
- EFO:0007336 (MONDO:equivalentTo)
- UMLS:C1260327 (MONDO:equivalentTo)
- DOID:7146 (MONDO:equivalentTo)
ordo_disorder, gard_rare, otar, rare, nord_rare, orphanet_rare
http://identifiers.org/mesh/D054752
http://purl.obolibrary.org/obo/NCIT_C6921
http://www.orpha.net/ORDO/Orphanet_86897
http://linkedlifedata.com/resource/umls/id/C1260327
http://purl.obolibrary.org/obo/DOID_7146
http://identifiers.org/medgen/266041
http://identifiers.org/snomedct/724649000