A neoplastic proliferation of Langerhans cells with overtly malignant cytologic features. It can be considered a higher grade variant of Langerhans cell histiocytosis (LCH) and it can present de novo or progress from antecedent LCH. (WHO, 2001) [ NCIT:C6921 ]

Synonyms: Langerhans cell sarcoma sarcoma of Langerhans cell

This is just here as a test because I lose it

Term information

database cross reference
  • SCTID:724649000 (MONDO:equivalentTo)
  • ONCOTREE:LCS (MONDO:equivalentTo)
  • MEDGEN:266041 (MONDO:equivalentTo)
  • NCIT:C6921 (MONDO:exact-label-match)
  • MESH:D054752 (Orphanet:86897/e)
  • Orphanet:86897 (MONDO:equivalentTo)
  • GARD:10491 (MONDO:GARD)
  • ICDO:9756/3 (NCIT:C6921)
  • NANDO:2200036 (https://orcid.org/0000-0003-0011-764X)
  • icd11.foundation:588958190 (Orphanet:86897)
  • EFO:0007336 (MONDO:equivalentTo)
  • UMLS:C1260327 (MONDO:equivalentTo)
  • DOID:7146 (MONDO:equivalentTo)
Subsets

ordo_disorder, gard_rare, otar, rare, nord_rare, orphanet_rare

abbreviation
LCS [ ONCOTREE:LCS ]

conformsTo

http://purl.obolibrary.org/obo/mondo/patterns/sarcoma.yaml

exactMatch

http://identifiers.org/mesh/D054752

http://purl.obolibrary.org/obo/NCIT_C6921

http://www.orpha.net/ORDO/Orphanet_86897

http://linkedlifedata.com/resource/umls/id/C1260327

http://purl.obolibrary.org/obo/DOID_7146

http://identifiers.org/medgen/266041

http://identifiers.org/snomedct/724649000

has related synonym

malignant Langerhans cell sarcoma

LCS

id

MONDO:0019480

seeAlso

https://rarediseases.info.nih.gov/diseases/10491/langerhans-cell-sarcoma