A usually indolent mature B-cell lymphoma, arising from the marginal zone of lymphoid tissues. It is characterized by the presence of small to medium sized atypical lymphocytes. It comprises three entities, according to the anatomic sites involved: extranodal marginal zone B-cell lymphoma of mucosa-associated lymphoid tissue, which affects extranodal sites (most often stomach, lung, skin, and ocular adnexa); nodal marginal zone B-cell lymphoma, which affects lymph nodes without evidence of extranodal disease; and splenic marginal zone B-cell lymphoma, which affects the spleen and splenic hilar lymph nodes, bone marrow, and often the peripheral blood. [ NCIT:C4341 ]
Synonyms: marginal zone B cell lymphoma marginal zone B-cell lymphoma MZBCL MZL lymphoma of marginal zone B cell marginal zone lymphoma
Term information
- DOID:0050748 (MONDO:equivalentTo)
- UMLS:C1367654 (MONDO:equivalentTo)
- EFO:1000630 (MONDO:equivalentTo)
- MEDGEN:277950 (MONDO:equivalentTo)
- ONCOTREE:MZL (MONDO:equivalentTo)
- ICDO:9699/3 (NCIT:C4341)
- Orphanet:300912 (MONDO:equivalentTo)
- NCIT:C4341 (MONDO:equivalentTo)
- SCTID:447100004 (MONDO:equivalentTo)
- GARD:13237 (MONDO:GARD)
gard_rare, otar, disease_grouping, rare, nord_rare, ordo_group_of_disorders
http://purl.obolibrary.org/obo/NCIT_C4341
http://purl.obolibrary.org/obo/DOID_0050748
http://identifiers.org/medgen/277950
http://www.orpha.net/ORDO/Orphanet_300912
http://identifiers.org/snomedct/447100004
http://linkedlifedata.com/resource/umls/id/C1367654