JSON

frontotemporal dementia

Go to external page http://purl.obolibrary.org/obo/MONDO_0017276

Frontotemporal dementia (FTD) comprises a group of neurodegenerative disorders, characterized by progressive changes in behavior, executive dysfunction and language impairment, as a result of degeneration of the medial prefrontal and frontoinsular cortices. Four clinical subtypes have been identified: semantic dementia, progressive non-fluent aphasia, behavioral variant FTD and right temporal lobar atrophy. [ Orphanet:282 ]

Synonyms: Wilhemsen-Lynch disease multiple system tauopathy with presenile dementia pallidopontonigral degeneration FTD frontotemporal lobar degeneration

This is just here as a test because I lose it

Term information

database cross reference
  • MESH:D057180 (Orphanet:282/e)
  • NANDO:1200548 (https://orcid.org/0000-0003-0011-764X)
  • UMLS:C0338451 (MONDO:equivalentTo)
  • DOID:9255 (MONDO:equivalentTo)
  • Orphanet:282 (MONDO:equivalentTo)
  • MedDRA:10068968 (Orphanet:282/e)
  • NCIT:C84719 (MONDO:equivalentTo)
  • GARD:8436 (MONDO:GARD)
  • MEDGEN:83266 (MONDO:equivalentTo)
  • icd11.foundation:831337417 (Orphanet:282)
Subsets

gard_rare, otar, disease_grouping, rare, ordo_group_of_disorders

abbreviation
FTD [ Orphanet:282 ]

abbreviation
MSTD [ GARD:0008436 ]

closeMatch

http://identifiers.org/meddra/10068968

exactMatch

http://purl.obolibrary.org/obo/NCIT_C84719

http://identifiers.org/mesh/D057180

http://identifiers.org/medgen/83266

http://linkedlifedata.com/resource/umls/id/C0338451

http://www.orpha.net/ORDO/Orphanet_282

http://purl.obolibrary.org/obo/DOID_9255

excluded subClassOf

http://purl.obolibrary.org/obo/MONDO_0003996

has related synonym

frontotemporal lobe dementia (FLDEM)

MSTD

id

MONDO:0017276