A malignant tumor arising from the endothelial cells of the blood vessels. Microscopically, it is characterized by frequently open vascular anastomosing and branching channels. The malignant cells that line the vascular channels are spindle or epithelioid and often display hyperchromatic nuclei. Angiosarcomas most frequently occur in the skin and breast. Patients with long-standing lymphedema are at increased risk of developing angiosarcoma. [ NCIT:C3088 ]
Synonyms: malignant angioendothelioma hemangiosarcoma, malignant blood vessel sarcoma vascular sarcoma angiosarcoma (disease) malignant hemangioendothelioma sarcoma of blood vessel angiosarcoma hemangiosarcoma
Term information
- NCIT:C3088 (MONDO:equivalentTo)
- HP:0200058 (MONDO:otherHierarchy)
- ICDO:9120/3 (NCIT:C3088)
- MEDGEN:42385 (MONDO:equivalentTo)
- ONCOTREE:ANGS (MONDO:equivalentTo)
- DOID:0001816 (MONDO:equivalentTo)
- GARD:20900 (MONDO:GARD)
- MedDRA:10002476 (Orphanet:263413/e)
- ICD9:171.9 (MONDO:relatedTo)
- UMLS:C0018923 (MONDO:equivalentTo)
- EFO:0003968 (MONDO:equivalentTo)
- MESH:D006394 (MONDO:equivalentTo)
- SCTID:403977003 (MONDO:equivalentTo)
- Orphanet:263413 (MONDO:equivalentTo)
gard_rare, ordo_disorder, otar, rare, nord_rare, orphanet_rare
http://purl.obolibrary.org/obo/NCIT_C3088
http://linkedlifedata.com/resource/umls/id/C0018923
http://identifiers.org/snomedct/403977003
http://identifiers.org/medgen/42385
http://www.orpha.net/ORDO/Orphanet_263413
http://identifiers.org/mesh/D006394
http://purl.obolibrary.org/obo/DOID_0001816