small intestinal enteropathy-associated T-cell lymphoma
Go to external page http://purl.obolibrary.org/obo/MONDO_0006418
An enteropathy-associated T-cell lymphoma arising from the small intestine, most commonly the jejunum or ileum. Patients usually present with abdominal pain, often associated with intestinal perforation. There is often a history of celiac disease. The lymphoma cells are usually medium-sized to large and form an ulcerating mucosal lesion with invasion of the small intestinal wall. Villous atrophy is present in the adjacent small intestinal mucosa. In a minority of cases the lymphoma cells are medium-sized and form a monomorphic infiltrate. [ NCIT:P378 ]
Synonyms: small intestinal EATL small intestinal enteropathy-type T-cell lymphoma enteropathy-associated T-cell lymphoma of small intestine small intestine enteropathy-associated T-cell lymphoma
Term information
- UMLS:C1519371 (MONDO:equivalentTo)
- NCIT:C39610 (MONDO:equivalentTo)
- MEDGEN:275445 (MONDO:equivalentTo)
- EFO:1000535 (MONDO:equivalentTo)
gard_rare, otar, rare
http://linkedlifedata.com/resource/umls/id/C1519371
http://purl.obolibrary.org/obo/NCIT_C39610
http://identifiers.org/medgen/275445
http://purl.obolibrary.org/obo/mondo/sparql/qc/general/qc-single-child.sparql