A primitive neuroectodermal tumor (small round blue cell tumor) of the thorax which can involve the periosteum, thoracic wall and/or pleura though it spares the lung parenchyma. [ NCIT:C7542 ]
Synonyms: peripheral neuroectodermal tumor of thoracopulmonary region PNET of thoracopulmonary region Askin's tumor Askin tumor peripheral neuroectodermal tumour of thoracopulmonary region small cell tumour of thoracopulmonary region small cell tumor of thoracopulmonary region Askin's tumour
Term information
- UMLS:C0877849 (MONDO:equivalentTo)
- NCIT:C7542 (MONDO:equivalentTo)
- MEDGEN:209112 (MONDO:equivalentTo)
- DOID:0050608 (MONDO:equivalentTo)
- ICDO:9365/3 (NCIT:C7542)
- MESH:C563168 (MONDO:equivalentTo)
- EFO:1000095 (MONDO:equivalentTo)
gard_rare, otar, rare, nord_rare
Editor note: in DO this is classified as Ewing sarcoma but we follow NCIT in placing as sibling
http://purl.obolibrary.org/obo/NCIT_C7542
http://identifiers.org/medgen/209112
http://linkedlifedata.com/resource/umls/id/C0877849
http://identifiers.org/mesh/C563168
http://purl.obolibrary.org/obo/DOID_0050608