A benign or malignant neuroendocrine neoplasm of the sympathetic nervous system that secretes catecholamines. It arises from the chromaffin cells of the adrenal medulla. Clinical presentation includes headaches, palpitations, chest and abdominal pain, hypertension, fever, and tremor. Microscopically, a characteristic nesting (zellballen) growth pattern is usually seen. Other growth patterns including trabecular pattern may also be present. [ NCIT:C3326 ]
Synonyms: PCC adrenal gland pheochromocytoma adrenal gland chromaffin paraganglioma adrenal medullary paraganglioma adrenal medullary pheochromocytoma adrenal gland Chromaffinoma adrenal pheochromocytoma Intraadrenal paraganglioma pheochromocytoma (adrenal) chromaffin paraganglioma of the adrenal gland adrenal gland paraganglioma
Term information
- DOID:0050892 (MONDO:equivalentTo)
- ICDO:8700/0 (NCIT:C3326)
- UMLS:C4551683 (MONDO:equivalentTo)
- NANDO:2200078 (https://orcid.org/0000-0003-0011-764X)
- MEDGEN:1636437 (MONDO:equivalentTo)
- NCIT:C3326 (MONDO:equivalentTo)
- EFO:0000239 (MONDO:equivalentTo)
gard_rare, otar, rare, nord_rare
http://purl.obolibrary.org/obo/DOID_0050892
http://purl.obolibrary.org/obo/NCIT_C3326
http://identifiers.org/medgen/1636437
http://linkedlifedata.com/resource/umls/id/C4551683