A low grade malignant neoplasm arising from the long bones. The tibia is the most frequently affected bone site. Patients present with swelling which may or may not be associated with pain. Morphologically, it is characterized by a biphasic pattern consisting of an epithelial and an osteofibrous component. The vast majority of cases recur if they are not treated with radical surgery. In a minority of cases the tumor may metastasize to other anatomic sites including lymph nodes, lungs, liver, brain, and skeleton. [ NCIT:C7644 ]
Synonyms: Extragnathic adamantinoma long bone adamantinoma adamantinoma of long bones adamantinoma of long bones (morphologic abnormality) adamantinoma, malignant adamantinoma
Term information
- MESH:C562741 (MONDO:equivalentTo)
- ONCOTREE:ADMA (MONDO:equivalentTo)
- NCIT:C7644 (MONDO:equivalentTo)
- SCTID:307609003 (MONDO:equivalentTo)
- OMIM:102660 (Orphanet:55881/e)
- ICD10CM:C40.2 (Orphanet:55881/ntbt)
- DOID:2775 (MONDO:equivalentTo)
- MESH:D050398 (Orphanet:55881/e)
- ICDO:9261/3 (NCIT:C7644)
- ICD9:170.9 (MONDO:relatedTo)
- UMLS:C0334556 (MONDO:equivalentTo)
- DOID:2776 (MONDO:equivalentTo)
- Orphanet:55881 (OMIM:102660)
- GARD:16660 (MONDO:GARD)
- MEDGEN:83163 (MONDO:equivalentTo)
gard_rare, ordo_disorder, otar, rare, nord_rare, orphanet_rare
http://purl.obolibrary.org/obo/DOID_2775
http://identifiers.org/mesh/D050398
http://purl.obolibrary.org/obo/DOID_2776
http://purl.obolibrary.org/obo/NCIT_C7644
http://identifiers.org/snomedct/307609003
http://identifiers.org/mesh/C562741
https://omim.org/entry/102660
http://linkedlifedata.com/resource/umls/id/C0334556
http://identifiers.org/medgen/83163
http://www.orpha.net/ORDO/Orphanet_55881