A benign or malignant neoplasm arising from paraganglia located along the sympathetic or parasympathetic nerves. Infrequently, it may arise outside the usual distribution of the sympathetic and parasympathetic paraganglia. Tumors arising from the adrenal gland medulla are called pheochromocytomas. Morphologically, paragangliomas usually display a nesting (Zellballen) growth pattern. There are no reliable morphologic criteria to distinguish between benign and malignant paragangliomas. The only definitive indicator of malignancy is the presence of regional or distant metastases. [ NCIT:C3308 ]
Synonyms: neoplasm of the paraganglion neoplasm of paraganglion tumor of the paraganglion tumor of paraganglion paraganglion tumour paraganglion tumor paraganglioma Paraganglionic tumour paraganglion neoplasm tumour of the paraganglion paragangliomas Paraganglionic neoplasm tumour of paraganglion Paraganglionic tumor
Term information
- ONCOTREE:PGNG (MONDO:equivalentTo)
- SCTID:127027008 (MONDO:equivalentTo)
- NCIT:C3308 (MONDO:equivalentTo)
- EFO:1000453 (MONDO:equivalentTo)
- ICD9:239.7 (MONDO:relatedTo)
- OMIMPS:168000 (https://orcid.org/0000-0002-6601-2165)
- DOID:0050773 (MONDO:equivalentTo)
- MEDGEN:10571 (MONDO:equivalentTo)
- ICDO:8680/1 (NCIT:C3308)
- MESH:D010235 (MONDO:equivalentTo)
- UMLS:C0030421 (MONDO:equivalentTo)
gard_rare, otar, rare
http://identifiers.org/snomedct/127027008
https://omim.org/phenotypicSeries/PS168000
http://identifiers.org/medgen/10571
http://purl.obolibrary.org/obo/DOID_0050773
http://identifiers.org/mesh/D010235
http://purl.obolibrary.org/obo/NCIT_C3308
http://linkedlifedata.com/resource/umls/id/C0030421
Term relations
- neuroendocrine neoplasm and disease has location some autonomic nervous system and disease arises from alteration in structure some neural crest cell